Procedure Description:

EPS With septostomy

Babies with congenital heart abnormalities can survive until they have corrective surgery with the use of a septostomy. The Rashkind operation or balloon atrial septostomy are other names for septostomy. Because it affects the atria, the two upper chambers of your baby's heart, the treatment is referred to as "atrial."

This is a percutaneous technique, which means that a medical professional will penetrate the skin with a needle and implant a catheter. A balloon within the catheter enlarges a hole that exists naturally in your baby's heart. Blood with more oxygen can mingle with blood with less oxygen through this opening.

The baby's body can then begin to circulate this partially oxygenated blood after it has left the heart. Your baby's blood would simply be oxygen-poor blood moving through their body without this pathway. Open cardiac surgery is not what a septostomy is. Rather, it's a stopgap measure to bridge the time between delivery and surgery.

Disease Overview:

Congenital heart defect

A congenital heart defect is an issue with the heart's structure that arises at birth. Certain congenital cardiac abnormalities in children are easily treated. Some congenital cardiac problems in children are more complicated and may need to be corrected over a number of years with multiple procedures.

Some children's congenital cardiac abnormalities are minor and do not require therapy. Other congenital cardiac problems in children are more complicated and may need many procedures over several years. Understanding your child's congenital heart problem will help you comprehend the situation and what to expect in the months and years ahead.

Disease Signs and Symptoms:

Congenital cardiac abnormalities that are serious are generally discovered immediately after birth or within the first few months of life. The following are possible signs and symptoms:

1- Skin that is pale grey or blue in hue (cyanosis)

2- Breathing quickly

3- Swelling in the legs, belly button, or eyelids

4- Shortness of breath during meals, resulting in inadequate weight gain

Congenital cardiac abnormalities that are less significant may not be detected until later in infancy. In older children, signs and symptoms of congenital cardiac abnormalities may include:

1- Getting out of breath easily during exercise or activity

2- Easily exhausted through physical exertion or exercise

3- Experiencing dizziness or fainting during physical activity

Hands, ankles, and feet swelling.

Disease Causes:

The majority of congenital heart abnormalities are caused by issues that arise during the development of the baby's heart before birth. Most congenital cardiac abnormalities have an unknown origin. Certain environmental and genetic risk factors, on the other hand, may have a role. They are as follows:

Rubella is a contagious disease that affect (German measles). Rubella can affect your baby's heart development if you get it while pregnant. Before you are pregnant, your doctor can check for immunity to this viral illness and vaccine you if you aren't.

Diabetes. By carefully regulating blood sugar levels before and during pregnancy, a woman who had diabetes before becoming pregnant can lower her risk of congenital heart abnormalities. Diabetes that develops during pregnancy (gestational diabetes) does not raise the chance of a heart abnormality in the newborn.

Medications. Certain drugs can cause birth problems, including congenital heart disorders, if used during pregnancy. Before attempting to conceive, give your doctor a thorough list of your drugs.

Thalidomide (Thalomid), angiotensin-converting enzyme (ACE) inhibitors, statins, the acne treatment isotretinoin (Absorica, Amnesteem, others), several epileptic medications, and some anxiety drugs are all known to raise the risk of congenital cardiac abnormalities.

Consumption of alcoholic beverages when pregnant. Consumption of alcoholic beverages during pregnancy raises the chance of congenital cardiac abnormalities.

Smoking. Quit smoking if you're a smoker. Smoking during pregnancy raises the likelihood of the baby developing a congenital heart condition.

Genetics and family history Congenital cardiac problems can run in families (i.e., they are inherited) and be linked to a genetic condition. Heart abnormalities are common in children who have an additional 21st chromosome (Down syndrome). Heart abnormalities can potentially be caused by a missing piece of genetic material (deletion) on chromosome 22.

Disease Diagnosis:

While the kid is still in the pregnancy, several congenital cardiac problems can be detected. A foetal ultrasound, a normal prenatal test used to monitor a baby's growth and development throughout pregnancy, can reveal signs of some cardiac problems.

If your kid seems blue, has abnormal growth, or your child's doctor hears an abnormal heart sound (murmur) while listening to your child's heart with a stethoscope after delivery, your child may have a congenital heart condition.

The majority of heart murmurs are benign, which means there is no heart defect present and the murmur is not harmful to your child's health. However, irregular blood flow to and from the heart can generate certain murmurs.

The following tests can be used to identify a congenital cardiac defect:

- Pulse oximetry is the measurement of oxygen saturation in the blood. This simple, noninvasive test determines how much oxygen is present in your child's blood. The amount of oxygen in your child's blood is measured by a sensor attached to his or her fingertip. A lack of oxygen might indicate that your child has a heart or lung condition.

- An EKG is a type of electrocardiogram (ECG or EKG). This noninvasive test monitors your child's heart's electrical activity. It can aid in the diagnosis of cardiac abnormalities or irregular heartbeats. On your baby's chest, sticky patches containing sensors (electrodes) are applied. The patches are connected to a computer through wires, which shows the results.

- Echocardiogram. An echocardiogram creates pictures of your or your child's heart in action using sound waves (ultrasound). The cardiac valves and heart muscle can be seen during an echocardiogram. A foetal echocardiography is an echocardiogram performed on a baby before birth.

- X-ray of the chest. A chest X-ray may be performed on your kid to see if the heart is enlarged or if the lungs contain excess blood or other fluid. These symptoms might indicate cardiac failure.

- Catheterization of the heart. A thin, flexible tube (catheter) is placed into a blood artery in the groyne area and directed to the heart during this examination. Catheterization can provide more specific information on heart function and blood flow to your child's doctor. During cardiac catheterization, several heart therapies are possible.

- Magnetic resonance imaging of the heart (MRI). The use of a cardiac MRI to diagnose and assess congenital heart abnormalities in adolescents and adults is becoming more widespread. A heart MRI provides three-dimensional images of the heart, allowing for precise measuring of the chambers.

Disease Treatment:

Treatment for congenital heart problems in children is determined by the kind of heart defect and its severity. A congenital cardiac abnormality may have no long-term consequences for your child's health and can thus be left untreated. Small holes, for example, may seal as your child grows older. Serious cardiac problems must be treated as soon as possible when they are discovered. Medication, cardiac surgeries, or a heart transplant may be used to treat the condition.

Medications: Medications can be used alone or in combination with a cardiac treatment to treat symptoms or consequences of a congenital heart problem. The following medications are used to treat congenital cardiac defects:

Medications for high blood pressure. Angiotensin-converting enzyme (ACE) inhibitors, angiotensin II receptor blockers (ARBs), and beta blockers are only a few examples.

Diuretics. This type of drug lowers the quantity of fluid in the body, easing the pressure on the heart.

Medications that help with heart rhythm. Anti-arrhythmic drugs assist to manage an irregular heartbeat (arrhythmia).

Surgical or non-surgical techniques

A cardiac treatment or surgery may be needed if your kid has a serious congenital heart problem. The following techniques and surgeries are used to address congenital cardiac defects:

Cardiac intervention in the foetus If a significant flaw is discovered before birth, there is a chance that a surgery can be performed during pregnancy to fix the condition or assist lessen the defect's complications as the child develops. Fetal cardiac intervention is a rare occurrence that occurs only in extremely limited conditions.

Catheterization of the heart. Congenital heart abnormalities are treated in some children and adults using thin, flexible tubes (catheters). Without open-heart surgery, cardiac catheterization can be performed to repair holes in the heart or narrowing regions.

A doctor inserts one or more catheters into a blood artery, usually in the groyne, and into the heart during cardiac catheterization. To fix the defect, tiny instruments are passed via the catheter to the heart. Some catheter operations must be performed in stages over several years.

Surgery on the heart is performed. To correct a congenital heart abnormality, your kid may require open-heart surgery or minimally invasive heart surgery.

A heart transplant is a procedure in which a person' A heart transplant may be required if a major cardiac defect cannot be fixed.